Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004812370 | SCV005437147 | uncertain significance | Hereditary factor IX deficiency disease | 2024-12-06 | reviewed by expert panel | curation | The F9 c.471T>C (p.Cys157=) variant is absent from males in population databases (gnomAD v2.1.1/gnomAD v3). The Cys157= synonymous variant is predicted to have no impact on splicing based on SpliceAI prediction. We are not aware of any cases of hemophilia B in the literature or in databases at this time. In summary, based on the evidence available at this time, the clinical significance of this variant is uncertain. ACMG/AMP criteria applied, as specified by the Coagulation Factor Deficiency Variant Curation Expert Panel for F9 (Released 10/5/2023): PM2_Supporting, BP4. |
Labcorp Genetics |
RCV001462720 | SCV001666645 | likely benign | Hereditary factor IX deficiency disease; Thrombophilia, X-linked, due to factor 9 defect | 2023-11-02 | criteria provided, single submitter | clinical testing |