Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001383452 | SCV001582602 | pathogenic | Fanconi anemia | 2020-01-03 | criteria provided, single submitter | clinical testing | This sequence change affects the initiator methionine of the FANCA mRNA. The next in-frame methionine is located at codon 116. This variant is expected to result in an absent or disrupted protein product. For these reasons, this variant has been classified as Pathogenic. Disruptions of the initiator codon (c.1A>T, c.1A>G, c.2T>A, and c.2T>C) have been reported in individuals affected with Fanconi anemia (PMID: 10090479, 16084127, 24584348, 15643609, 22778927, 23898106). The frequency data for this variant in the population databases is considered unreliable, as metrics indicate insufficient coverage at this position in the ExAC database. |