Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000469377 | SCV000549947 | uncertain significance | Fanconi anemia | 2024-01-04 | criteria provided, single submitter | clinical testing | This sequence change replaces histidine, which is basic and polar, with leucine, which is neutral and non-polar, at codon 207 of the FANCC protein (p.His207Leu). This variant is present in population databases (rs202038890, gnomAD 0.004%). This missense change has been observed in individual(s) with breast cancer and serous cystadenoma (PMID: 23028338, 28767289). ClinVar contains an entry for this variant (Variation ID: 409651). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) has been performed at Invitae for this missense variant, however the output from this modeling did not meet the statistical confidence thresholds required to predict the impact of this variant on FANCC protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Gene |
RCV000480838 | SCV000564975 | uncertain significance | not provided | 2023-03-29 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 23028338, 28767289, Gordon2000[Book]) |
Fulgent Genetics, |
RCV000766067 | SCV000897538 | uncertain significance | Fanconi anemia complementation group C | 2022-03-16 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV000469377 | SCV002535113 | uncertain significance | Fanconi anemia | 2021-05-07 | criteria provided, single submitter | curation | |
Ambry Genetics | RCV002365644 | SCV002658146 | uncertain significance | Hereditary cancer-predisposing syndrome | 2022-06-03 | criteria provided, single submitter | clinical testing | The p.H207L variant (also known as c.620A>T), located in coding exon 6 of the FANCC gene, results from an A to T substitution at nucleotide position 620. The histidine at codon 207 is replaced by leucine, an amino acid with similar properties. This alteration has been reported in a cohort of breast cancer families (Thompson ER et al. PLoS Genet., 2012 Sep;8:e1002894). This amino acid position is well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Natera, |
RCV000469377 | SCV002081241 | uncertain significance | Fanconi anemia | 2018-09-17 | no assertion criteria provided | clinical testing |