Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
DASA | RCV002052293 | SCV002318965 | likely pathogenic | Marfan syndrome | 2022-03-25 | criteria provided, single submitter | clinical testing | The variant is located in a mutational hot spot and/or critical and well-established functional domain (EGF_CA; cEGF) - PM1. This variant is not present in population databases (rs956678986- gnomAD; ABraOM no frequency - http://abraom.ib.usp.br.) - PM2. Missense variant in FBN1 that has a low rate of benign missense variation and in which missense variants are a common mechanism of disease - PP2. Multiple lines of computational evidence support a deleterious effect on the gene or gene product - PP3. In summary, the currently available evidence indicates that the variant is likely pathogenic |