Total submissions: 12
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Illumina Laboratory Services, |
RCV000262990 | SCV000360795 | likely benign | Craniosynostosis syndrome | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000315856 | SCV000360796 | likely benign | Jackson-Weiss syndrome | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000372710 | SCV000360797 | likely benign | Isolated coronal synostosis | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000275939 | SCV000360798 | likely benign | Saethre-Chotzen syndrome | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000334006 | SCV000360799 | likely benign | Levy-Hollister syndrome | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000386154 | SCV000360800 | likely benign | Crouzon syndrome | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000294254 | SCV000360801 | likely benign | Pfeiffer syndrome | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000346874 | SCV000360802 | likely benign | Beare-Stevenson cutis gyrata syndrome | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000385163 | SCV000360803 | likely benign | Acrocephalosyndactyly type I | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Gene |
RCV003148705 | SCV003837438 | uncertain significance | not provided | 2022-09-06 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation, as the last 274 amino acids are replaced with 39 different amino acids; however, the majority of reported variants in this gene result in a gain-of-function; Has not been previously published as pathogenic or benign to our knowledge; Reported using an alternate transcript of the gene |
Ce |
RCV003148705 | SCV004134762 | likely benign | not provided | 2023-05-01 | criteria provided, single submitter | clinical testing | FGFR2: BS1 |
Clinical Genomics Laboratory, |
RCV004558616 | SCV005047087 | uncertain significance | FGFR2-related disorder | 2024-04-02 | criteria provided, single submitter | clinical testing | The FGFR2 c.2045del p.Lys682Argfs* variant was found at a near heterozygous allelic fraction consistent with germline origin. This variant, to our knowledge, has not been reported in the medical literature. This variant has been reported in the ClinVar database as an uncertain significance germline variant by one submitter (ClinVar ID: 298992). This variant causes a frameshift by deleting 1 nucleotide, leading to a premature termination codon; however, because this occurs in the last exon, this is not predicted to lead to nonsense mediated decay. Due to limited information and based on ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of this variant is uncertain at this time. |