Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV002251274 | SCV002521857 | uncertain significance | Glycogen storage disease, type II | 2022-05-22 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.65; 3Cnet: 0.93). Different missense changes at the same codon (p.His612Gln, p.His612Tyr) have been reported to be associated with GAA- related disorder (ClinVar ID: VCV000972801 / PMID: 16917947, 19588081). However the evidence of pathogenicity is insufficient at this time. Therefore, this variant is classified as uncertain significanceaccording to the recommendation of ACMG/AMP guideline. |