Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV000193049 | SCV000247470 | uncertain significance | not specified | 2014-06-19 | criteria provided, single submitter | clinical testing | |
Clinical Genomics, |
RCV002463660 | SCV002605069 | uncertain risk allele | Maturity onset diabetes mellitus in young | criteria provided, single submitter | research | Potent mutations in GCK gene is associated with poor secretion of insulin. Its associated with milder forms of diabetes, which can be controlled by diet . However, there is no sufficient evidence to ascertain the significance of rs779460424 in MODY, yet. | |
Fulgent Genetics, |
RCV002478669 | SCV002786307 | uncertain significance | Type 2 diabetes mellitus; Hyperinsulinism due to glucokinase deficiency; Maturity-onset diabetes of the young type 2; Permanent neonatal diabetes mellitus 1 | 2022-05-03 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003765221 | SCV004655884 | uncertain significance | not provided | 2023-06-06 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt GCK protein function. ClinVar contains an entry for this variant (Variation ID: 211075). This variant has not been reported in the literature in individuals affected with GCK-related conditions. This variant is present in population databases (rs779460424, gnomAD 0.004%). This sequence change replaces aspartic acid, which is acidic and polar, with asparagine, which is neutral and polar, at codon 262 of the GCK protein (p.Asp262Asn). |