Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004520631 | SCV005032543 | pathogenic | Maturity onset diabetes mellitus in young | 2019-07-18 | criteria provided, single submitter | clinical testing | The c.905delT pathogenic mutation, located in coding exon 8 of the GCK gene, results from a deletion of one nucleotide at nucleotide position 905, causing a translational frameshift with a predicted alternate stop codon (p.V302Gfs*51). This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |