Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002276541 | SCV002567546 | pathogenic | not provided | 2022-02-21 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); Also known as p.C83X (c.346C>A) using alternative nomenclature; This variant is associated with the following publications: (PMID: 25525159, 28498917, 19169479, 29748515, 17405847, 21525302, 15536163) |
OMIM | RCV000009191 | SCV000029408 | pathogenic | Laron-type isolated somatotropin defect | 2005-01-01 | no assertion criteria provided | literature only |