Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV000009170 | SCV002526686 | uncertain significance | Short stature due to partial GHR deficiency | 2022-05-17 | criteria provided, single submitter | clinical testing | Criteria applied: PS4_SUP |
Labcorp Genetics |
RCV002512935 | SCV003525721 | uncertain significance | not provided | 2022-01-01 | criteria provided, single submitter | clinical testing | This sequence change replaces glutamic acid, which is acidic and polar, with aspartic acid, which is acidic and polar, at codon 242 of the GHR protein (p.Glu242Asp). This variant is present in population databases (rs45588036, gnomAD 0.008%). This missense change has been observed in individual(s) with growth hormone insensitivity (PMID: 7565946). This variant is also known as p.Glu224Asp. ClinVar contains an entry for this variant (Variation ID: 8638). Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C35". The aspartic acid amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
OMIM | RCV000009170 | SCV000029387 | pathogenic | Short stature due to partial GHR deficiency | 1995-10-26 | no assertion criteria provided | literature only |