Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV001783380 | SCV002024843 | pathogenic | Glycine encephalopathy | 2019-09-04 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001783380 | SCV002243131 | pathogenic | Glycine encephalopathy | 2021-04-29 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has been observed in individual(s) with GLDC-related conditions (PMID: 27362913). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Tyr725*) in the GLDC gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in GLDC are known to be pathogenic (PMID: 16601880). |