Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Color Diagnostics, |
RCV000771152 | SCV000902991 | likely benign | Hereditary cancer-predisposing syndrome | 2017-03-28 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001712748 | SCV001941542 | benign | not provided | 2015-09-15 | criteria provided, single submitter | clinical testing | |
Department of Pathology and Laboratory Medicine, |
RCV001355760 | SCV001550729 | uncertain significance | Lynch syndrome | no assertion criteria provided | clinical testing | The MSH6 c.*11T>C variant was not identified in the literature nor was it identified in the ClinVar or UMD-LSDB databases. The variant was identified in dbSNP (ID: rs757708396). The variant was identified in control databases in 2 of 245696 chromosomes at a frequency of 0.000008 (Genome Aggregation Database Feb 27, 2017). The variant was observed in the following populations: Latino in 1 of 33520 chromosomes (freq: 0.00003) and European in 1 of 111462 chromosomes (freq: 0.000009), but not in the African, Other, Ashkenazi Jewish, East Asian, Finnish, or South Asian populations. The variant occurs outside of the splicing consensus sequence and in silico or computational prediction software programs (SpliceSiteFinder, MaxEntScan, NNSPLICE, GeneSplicer) do not predict a difference in splicing. In summary, based on the above information, the clinical significance of this variant cannot be determined with certainty at this time. This variant is classified as a variant of uncertain significance. | |
Prevention |
RCV004535897 | SCV004715594 | likely benign | MSH6-related disorder | 2020-12-08 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |