Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000234013 | SCV000283724 | likely benign | Hereditary nonpolyposis colorectal neoplasms | 2024-07-23 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV000580239 | SCV000685208 | uncertain significance | Hereditary cancer-predisposing syndrome | 2019-05-17 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000580239 | SCV001173034 | uncertain significance | Hereditary cancer-predisposing syndrome | 2019-07-31 | criteria provided, single submitter | clinical testing | The p.S550C variant (also known as c.1649C>G), located in coding exon 4 of the MSH6 gene, results from a C to G substitution at nucleotide position 1649. The serine at codon 550 is replaced by cysteine, an amino acid with dissimilar properties. This amino acid position is well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Gene |
RCV004767182 | SCV005375811 | uncertain significance | not provided | 2023-11-10 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Identified in an individual with breast cancer (PMID: 35402282); This variant is associated with the following publications: (PMID: 17531815, 21120944, 35402282) |