Total submissions: 9
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000167307 | SCV000218154 | likely benign | Hereditary cancer-predisposing syndrome | 2014-12-12 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Counsyl | RCV000411260 | SCV000488380 | likely benign | Lynch syndrome 5 | 2016-03-11 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001721092 | SCV000531748 | likely benign | not provided | 2020-03-06 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000531634 | SCV000624835 | likely benign | Hereditary nonpolyposis colorectal neoplasms | 2023-11-24 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV000167307 | SCV000685373 | likely benign | Hereditary cancer-predisposing syndrome | 2016-08-19 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV000167307 | SCV002527992 | likely benign | Hereditary cancer-predisposing syndrome | 2021-10-05 | criteria provided, single submitter | curation | |
Myriad Genetics, |
RCV000411260 | SCV004018895 | benign | Lynch syndrome 5 | 2023-03-28 | criteria provided, single submitter | clinical testing | This variant is considered benign. This variant is a silent/synonymous amino acid change and it is not expected to impact splicing. |
All of Us Research Program, |
RCV003995580 | SCV004835023 | likely benign | Lynch syndrome | 2023-08-08 | criteria provided, single submitter | clinical testing | |
Department of Pathology and Laboratory Medicine, |
RCV001353761 | SCV000592630 | likely benign | Carcinoma of colon | no assertion criteria provided | clinical testing | The MSH6, p.Thr1085Thr variant was identified only in dbSNP (ID: rs371568610) with a minor allele frequency of 0.0004 (1000 Genomes Project). It was not identified in NHLBI Exome Sequencing Project (Exome Variant Server), Exome Aggregation Consortium (ExAC) database, HGMD, COSMIC, MutDB, “Mismatch Repair Genes Variant Database”, “MMR Gene Unclassified Variants Database”, InSiGHT Colon Cancer Gene Variant Database, “Zhejiang Colon Cancer Database”, the ClinVar database, GeneInsight VariantWire database and UMD. The p.Thr1085Thr variant is not expected to have clinical significance because it does not result in a change of amino acid and is not located in a known consensus splice site. In addition, in silico or computational prediction software programs (SpliceSiteFinder, MaxEntScan, NNSPLICE, GeneSplicer, HumanSpliceFinder) do not predict a difference in splicing. In summary, based on the above information, the clinical significance of this variant cannot be determined with certainty at this time although we would lean towards a more benign role for this variant. This variant is classified as predicted benign. |