Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
SIB Swiss Institute of Bioinformatics | RCV000755725 | SCV000883211 | uncertain significance | Choroidal dystrophy, central areolar, 1 | 2018-10-15 | criteria provided, single submitter | curation | This variant is interpreted as Uncertain Significance - Insufficient Evidence, for Choroidal dystrophy, central areolar 1, autosomal recessive. The following ACMG Tag(s) were applied: PM2 => Absent from controls (or at extremely low frequency if recessive) in Exome Sequencing Project, 1000 Genomes Project, or Exome Aggregation Consortium. PP1 => Cosegregation with disease in multiple affected family members in a gene definitively known to cause the disease (https://www.ncbi.nlm.nih.gov/pubmed/22695961). PP3 => Multiple lines of computational evidence support a deleterious effect on the gene or gene product. PM1-Supporting => PM1 downgraded in strength to Supporting. |
OMIM | RCV000755725 | SCV000622099 | pathogenic | Choroidal dystrophy, central areolar, 1 | 2023-08-18 | no assertion criteria provided | literature only |