Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001372655 | SCV001569335 | uncertain significance | Cone-rod dystrophy 6; Leber congenital amaurosis 1 | 2020-09-16 | criteria provided, single submitter | clinical testing | This sequence change replaces methionine with valine at codon 218 of the GUCY2D protein (p.Met218Val). The methionine residue is highly conserved and there is a small physicochemical difference between methionine and valine. This variant is present in population databases (rs780953815, ExAC 0.004%). This variant has not been reported in the literature in individuals with GUCY2D-related conditions. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |