Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
IUMS Hospital Medical Genetics Lab, |
RCV004799694 | SCV005420949 | likely pathogenic | Hereditary hemolytic uremic syndrome | 2018-11-09 | no assertion criteria provided | research | A combination of the splice site mutation (IVS9-3 T > C) and the missense mutation NM_000186.4 c.1207G>C (p.G403R) in CFH gene in heterozygote state is likely associated with the disease. Based on ACMG criteria, the variation c.1204C>T (p.H402Y) (one aa before the current variation) is classified as a benign variation (https://www.ncbi.nlm.nih.gov/clinvar/variation/294490/). However, the association of the splice site mutation (IVS9-3 T > C) has already been reported with p.H402Y in heterozygote state has already been reported. |