Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003562321 | SCV004293867 | uncertain significance | not provided | 2024-02-18 | criteria provided, single submitter | clinical testing | This sequence change replaces glutamic acid, which is acidic and polar, with aspartic acid, which is acidic and polar, at codon 635 of the CFH protein (p.Glu635Asp). This variant is not present in population databases (gnomAD no frequency). This missense change has been observed in individual(s) with atypical hemolytic uremic syndrome (PMID: 17599974). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV005013028 | SCV005630462 | uncertain significance | Basal laminar drusen; Factor H deficiency; Hemolytic uremic syndrome, atypical, susceptibility to, 1; Age related macular degeneration 4 | 2024-02-05 | criteria provided, single submitter | clinical testing |