Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Diagnosis and Therapy of Lysosomal Disorders, |
RCV000790542 | SCV000929877 | uncertain significance | Mucopolysaccharidosis type 1 | 2019-01-01 | criteria provided, single submitter | literature only | PM2: Absent from GnomAD. PP3:multiple lines of computational evidence supporting a deleterious effect (DANN, MutationTaster, GERP, SIFT) |
Fulgent Genetics, |
RCV005036125 | SCV005667788 | likely pathogenic | Mucopolysaccharidosis, MPS-I-S; Hurler syndrome; Mucopolysaccharidosis, MPS-I-H/S | 2024-01-10 | criteria provided, single submitter | clinical testing |