Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV002251142 | SCV002521587 | uncertain significance | Factor I deficiency | 2022-05-22 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.87; 3Cnet: 3CNET). Same nucleotide change resulting in same amino acid change has been previously reported to be associated with CFI related disorder (PMID: 19065647). However, the evidence of pathogenicity is insufficient at this time. Therefore, this variant is classified as uncertain significanceaccording to the recommendation of ACMG/AMP guideline. |
Mayo Clinic Laboratories, |
RCV004793753 | SCV005413658 | likely pathogenic | not provided | 2024-02-13 | criteria provided, single submitter | clinical testing | PP3, PM2, PS3_supporting, PS4 |