Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genomics, |
RCV000258877 | SCV004174217 | uncertain significance | Diabetes mellitus, permanent neonatal 4 | criteria provided, single submitter | research | Potent mutations in the INS gene can cause early onset diabetes mellitus which is insulin dependent. May have poor response to sulfonylureas, mutations in this gene can cause beta cell destruction. c.187+241G>A (rs886041083) is a intronic variant seen to be associated with Neonatal diabetes. | |
OMIM | RCV000258877 | SCV000328652 | pathogenic | Diabetes mellitus, permanent neonatal 4 | 2020-12-01 | no assertion criteria provided | literature only |