Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV000502540 | SCV000595251 | uncertain significance | not specified | 2017-04-27 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001857113 | SCV002201695 | uncertain significance | not provided | 2021-09-20 | criteria provided, single submitter | clinical testing | Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Not Available"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Not Available"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. ClinVar contains an entry for this variant (Variation ID: 435516). This variant has not been reported in the literature in individuals affected with INSR-related conditions. This variant is present in population databases (rs775854644, ExAC no frequency). This sequence change replaces isoleucine with threonine at codon 1137 of the INSR protein (p.Ile1137Thr). The isoleucine residue is highly conserved and there is a moderate physicochemical difference between isoleucine and threonine. |
Fulgent Genetics, |
RCV002476006 | SCV002778981 | uncertain significance | Insulin-resistant diabetes mellitus AND acanthosis nigricans; Hyperinsulinism due to INSR deficiency; Leprechaunism syndrome; Rabson-Mendenhall syndrome | 2021-12-30 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV001857113 | SCV003815637 | uncertain significance | not provided | 2021-02-02 | criteria provided, single submitter | clinical testing |