Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Department Of Endocrinology, |
RCV003329144 | SCV004031465 | uncertain significance | Maturity-onset diabetes of the young type 4 | 2023-08-15 | criteria provided, single submitter | clinical testing | A heterozygous missense variation in exon 1 of the PDX1 gene (chr13:g.27920501G>T) that results in the amino acid substitution of Cysteine for Tryptophan at codon 121. The variant was found to be damaging by MutationTaster 2 and SIFT, and probably damaging by PolyPhen 2. The variant has not been reported in the 1000 genomes and gnomAD. The reference codon is conserved across species. PM2 PP3. |