Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Genetics, |
RCV005215803 | SCV005688774 | likely pathogenic | Glanzmann thrombasthenia 2 | criteria provided, single submitter | clinical testing | Parents are heterozygote genotype indicating carrier of this variant. The B3 integrin gene, also known as ITGB3 (Integrin Subunit Beta 3), encodes a protein that is a crucial part of the integrin family—specifically, the glycoprotein IIb/IIIa complex (GPIIb/IIIa), which is essential for platelet aggregation and blood clotting. Mutations in this gene can lead to various bleeding disorders, most notably Glanzmann thrombasthenia. |