Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003073783 | SCV003448236 | likely benign | Alagille syndrome due to a JAG1 point mutation | 2023-04-24 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV003171004 | SCV003863897 | uncertain significance | Cardiovascular phenotype | 2022-12-16 | criteria provided, single submitter | clinical testing | The p.D189G variant (also known as c.566A>G), located in coding exon 4 of the JAG1 gene, results from an A to G substitution at nucleotide position 566. The aspartic acid at codon 189 is replaced by glycine, an amino acid with similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |