Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001837169 | SCV005837681 | uncertain significance | Hypogonadotropic hypogonadism 1 with or without anosmia | 2024-10-17 | criteria provided, single submitter | clinical testing | This sequence change affects an acceptor splice site in intron 7 of the ANOS1 gene. RNA analysis indicates that disruption of this splice site induces altered splicing and likely results in the loss of 8 amino acid residue(s), but is expected to preserve the integrity of the reading-frame. This variant is not present in population databases (gnomAD no frequency). Disruption of this splice site has been observed in individual(s) with clinical features of Kallmann syndrome (PMID: 36039580, 36859276). ClinVar contains an entry for this variant (Variation ID: 1341676). Studies have shown that disruption of this splice site results in the activation of a cryptic splice site in exon 8 (PMID: 36859276). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Department of Surgery, |
RCV001837169 | SCV002097589 | likely pathogenic | Hypogonadotropic hypogonadism 1 with or without anosmia | 2022-02-14 | no assertion criteria provided | research |