Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004626563 | SCV005122525 | uncertain significance | Cardiovascular phenotype | 2024-04-04 | criteria provided, single submitter | clinical testing | The p.T6I variant (also known as c.17C>T), located in coding exon 1 of the KCNE1 gene, results from a C to T substitution at nucleotide position 17. The threonine at codon 6 is replaced by isoleucine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |
Roden Lab, |
RCV004780742 | SCV005393285 | not provided | Long QT syndrome 5 | no assertion provided | in vitro |