Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003554882 | SCV004292363 | pathogenic | not provided | 2023-04-25 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Ala1064*) in the LAMB3 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in LAMB3 are known to be pathogenic (PMID: 11023379, 16473856). Information on the frequency of this variant in the gnomAD database is not available, as this variant may be reported differently in the database. This premature translational stop signal has been observed in individual(s) with junctional epidermolysis bullosa (PMID: 11810295). For these reasons, this variant has been classified as Pathogenic. |
Fulgent Genetics, |
RCV005014764 | SCV005645556 | pathogenic | Amelogenesis imperfecta type 1A; Junctional epidermolysis bullosa gravis of Herlitz; Junctional epidermolysis bullosa, non-Herlitz type | 2024-04-08 | criteria provided, single submitter | clinical testing |