Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ARUP Laboratories, |
RCV001001285 | SCV001158464 | uncertain significance | Autosomal recessive limb-girdle muscular dystrophy type 2E | 2019-06-02 | criteria provided, single submitter | clinical testing | The SGCB c.152G>A; p.Arg51His variant (rs143751283), to our knowledge, is not reported in the medical literature or gene-specific databases. This variant is found on only eight chromosomes (8/277198 alleles) in the Genome Aggregation Database. The arginine at codon 51 is highly conserved, but computational analyses (SIFT: tolerated, PolyPhen-2: damaging) predict conflicting effects of this variant on protein structure/function. However, due to limited information, the clinical significance of the p.Arg51His variant is uncertain at this time. |
Natera, |
RCV001001285 | SCV001462207 | uncertain significance | Autosomal recessive limb-girdle muscular dystrophy type 2E | 2020-03-10 | no assertion criteria provided | clinical testing |