Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001069412 | SCV001234576 | pathogenic | Autosomal recessive limb-girdle muscular dystrophy type 2E | 2023-12-07 | criteria provided, single submitter | clinical testing | This sequence change affects the initiator methionine of the SGCB mRNA. The next in-frame methionine is located at codon 22. This variant is not present in population databases (gnomAD no frequency). Disruption of the initiator codon has been observed in individuals with autosomal recessive limb-girdle muscular dystrophy (PMID: 12566530, 15938573, 25135358, 25862795). It has also been observed to segregate with disease in related individuals. ClinVar contains an entry for this variant (Variation ID: 862654). For these reasons, this variant has been classified as Pathogenic. |