Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000875053 | SCV001017322 | benign | Familial Mediterranean fever | 2024-01-16 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV001193205 | SCV001361911 | uncertain significance | not specified | 2019-05-31 | criteria provided, single submitter | clinical testing | Variant summary: MEFV c.1610+10G>T alters a non-conserved nucleotide located close to a canonical splice site and therefore could affect mRNA splicing, leading to a significantly altered protein sequence. 5/5 computational tools predict no significant impact on normal splicing. However, these predictions have yet to be confirmed by functional studies. The variant allele was found at a frequency of 0.00029 in 251394 control chromosomes. This frequency is not significantly higher than expected for a pathogenic variant in MEFV causing Familial Mediterranean Fever (0.00029 vs 0.022), allowing no conclusion about variant significance. To our knowledge, no occurrence of c.1610+10G>T in individuals affected with Familial Mediterranean Fever and no experimental evidence demonstrating its impact on protein function have been reported. No clinical diagnostic laboratories have submitted clinical-significance assessments for this variant to ClinVar after 2014. Based on the evidence outlined above, the variant was classified as uncertain significance. |
Gene |
RCV001692309 | SCV001907004 | benign | not provided | 2015-03-03 | criteria provided, single submitter | clinical testing | |
Natera, |
RCV000875053 | SCV001458298 | uncertain significance | Familial Mediterranean fever | 2020-01-17 | no assertion criteria provided | clinical testing |