Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000223214 | SCV000279051 | pathogenic | not provided | 2014-07-03 | criteria provided, single submitter | clinical testing | The c.1759+1 G>A mutation has not been published as a mutation, nor has it been reported as a benign polymorphism to our knowledge. The c.1759+1 G>A variant was not observed in approximately 6,500 individuals of European and African American ancestry in the NHLBI Exome Sequencing Project, indicating it is not a common benign variant in these populations. Several in-silico splice prediction models predict that c.1759+1 G>A destroys the canonical splice donor site of intron 8. Other splice site mutations in exon 8 of the MEFV gene have been published, according to the Human Gene Mutation Database (Stenson et al., 2009). |
Greenwood Genetic Center Diagnostic Laboratories, |
RCV000223214 | SCV003932180 | uncertain significance | not provided | 2023-03-07 | criteria provided, single submitter | clinical testing | PM2 |