Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001388596 | SCV001589650 | pathogenic | Hereditary nonpolyposis colorectal neoplasms | 2020-06-21 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Tyr815*) in the MSH2 gene. It is expected to result in an absent or disrupted protein product. For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in MSH2 are known to be pathogenic (PMID: 15849733, 24362816). This variant has not been reported in the literature in individuals with MSH2-related conditions. This variant is not present in population databases (ExAC no frequency). |
Ambry Genetics | RCV002456607 | SCV002736761 | pathogenic | Hereditary cancer-predisposing syndrome | 2018-05-30 | criteria provided, single submitter | clinical testing | The p.Y815* pathogenic mutation (also known as c.2445T>A), located in coding exon 14 of the MSH2 gene, results from a T to A substitution at nucleotide position 2445. This changes the amino acid from a tyrosine to a stop codon within coding exon 14. This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |
Myriad Genetics, |
RCV003451684 | SCV004188941 | pathogenic | Lynch syndrome 1 | 2023-08-08 | criteria provided, single submitter | clinical testing | This variant is considered pathogenic. This variant creates a termination codon and is predicted to result in premature protein truncation. |
de |
RCV003451684 | SCV004022227 | pathogenic | Lynch syndrome 1 | 2023-07-21 | no assertion criteria provided | research | The variant NM_000251.3:c.2445T>A (chr2:47478506) in MSH2 was detected in 5 heterozygotes out of 58K WGS Icelanders (MAF= 0,004%). Following imputation in a set of 166K Icelanders (12 imputed heterozygotes) we observed an association with colorectal cancer using 4991 cases and 314812 controls (OR= 14.51, P= 1.01e-04). This variant has been reported in ClinVar previously as pathogenic. Based on ACMG criteria (PVS1, PS4) this variant classifies as pathogenic. |