Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004589504 | SCV005080711 | likely pathogenic | not provided | 2024-02-06 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 25525159, 30047259, 20682747, 12522554, 27538056, 34011573, 10726846, 12859411) |
OMIM | RCV000011811 | SCV000032044 | pathogenic | Severe X-linked myotubular myopathy | 2003-08-01 | no assertion criteria provided | literature only |