Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003516004 | SCV004334563 | pathogenic | Methylcobalamin deficiency type cblG | 2023-12-04 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Leu5Profs*16) in the MTR gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in MTR are known to be pathogenic (PMID: 9683607, 12068375). This variant is present in population databases (rs752220849, gnomAD 0.0009%). This premature translational stop signal has been observed in individual(s) with methylcobalamin deficiency (PMID: 12068375). For these reasons, this variant has been classified as Pathogenic. |