Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001758731 | SCV001996980 | uncertain significance | not provided | 2019-12-17 | criteria provided, single submitter | clinical testing | Not observed at a significant frequency in large population cohorts (Lek et al., 2016); In silico analysis, which includes protein predictors and evolutionary conservation, supports a deleterious effect; Has not been previously published as pathogenic or benign to our knowledge |
Labcorp Genetics |
RCV002540417 | SCV003031801 | uncertain significance | Methylcobalamin deficiency type cblG | 2022-09-12 | criteria provided, single submitter | clinical testing | This sequence change replaces alanine, which is neutral and non-polar, with glutamic acid, which is acidic and polar, at codon 442 of the MTR protein (p.Ala442Glu). This variant is present in population databases (rs770004849, gnomAD 0.007%). This variant has not been reported in the literature in individuals affected with MTR-related conditions. ClinVar contains an entry for this variant (Variation ID: 1311222). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt MTR protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV004641689 | SCV005146692 | uncertain significance | Inborn genetic diseases | 2024-06-17 | criteria provided, single submitter | clinical testing | The c.1325C>A (p.A442E) alteration is located in exon 14 (coding exon 14) of the MTR gene. This alteration results from a C to A substitution at nucleotide position 1325, causing the alanine (A) at amino acid position 442 to be replaced by a glutamic acid (E). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |