Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV001823697 | SCV002073328 | uncertain significance | Methylmalonic aciduria due to methylmalonyl-CoA mutase deficiency | criteria provided, single submitter | clinical testing | The missense variant p.D738G in MUT (NM_000255.4) has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.D738G variant is novel (not in any individuals) in gnomAD Exomes and is novel (not in any individuals) in 1000 Genomes. In-silico tools predict are contradictory in their predictions (SIFT-damaging, Polyphen-2-Tolerated) and the residue is conserved across species. For these reasons, this variant has been classified as Uncertain Significance. |