Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001370413 | SCV001566894 | benign | Gorlin syndrome | 2024-05-09 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004037471 | SCV005034216 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-12-04 | criteria provided, single submitter | clinical testing | The p.A1061V variant (also known as c.3182C>T), located in coding exon 19 of the PTCH1 gene, results from a C to T substitution at nucleotide position 3182. The alanine at codon 1061 is replaced by valine, an amino acid with similar properties. This amino acid position is well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |