Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000460060 | SCV000549078 | likely benign | Gorlin syndrome | 2024-06-11 | criteria provided, single submitter | clinical testing | |
Gene |
RCV002259341 | SCV002538730 | uncertain significance | not provided | 2021-12-20 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
St. |
RCV000460060 | SCV002584639 | uncertain significance | Gorlin syndrome | 2022-09-20 | criteria provided, single submitter | clinical testing | The PTCH1 c.329G>C (p.Gly110Ala) missense change has a maximum subpopulation frequency of 0.0016% in gnomAD v2.1.1 (https://gnomad.broadinstitute.org/). The in silico tool REVEL is inconclusive about a pathogenic or benign effect of this variant on protein function, and to our knowledge functional studies have not been performed. To our knowledge, this variant has not been reported in individuals with nevoid basal cell carcinoma syndrome. In summary, the evidence currently available is insufficient to determine the clinical significance of this variant. It has therefore been classified as of uncertain significance. |
Ambry Genetics | RCV002323723 | SCV002607053 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-02-15 | criteria provided, single submitter | clinical testing | The p.G110A variant (also known as c.329G>C), located in coding exon 2 of the PTCH1 gene, results from a G to C substitution at nucleotide position 329. The glycine at codon 110 is replaced by alanine, an amino acid with similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Based on the available evidence, the clinical significance of this alteration remains unclear. |
Baylor Genetics | RCV003463913 | SCV004206574 | uncertain significance | Basal cell carcinoma, susceptibility to, 1 | 2023-09-05 | criteria provided, single submitter | clinical testing |