Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002001828 | SCV002214889 | benign | Gorlin syndrome | 2024-09-27 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002458844 | SCV002617602 | uncertain significance | Hereditary cancer-predisposing syndrome | 2022-01-15 | criteria provided, single submitter | clinical testing | The p.I1161V variant (also known as c.3481A>G), located in coding exon 21 of the PTCH1 gene, results from an A to G substitution at nucleotide position 3481. The isoleucine at codon 1161 is replaced by valine, an amino acid with highly similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |