Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002349325 | SCV002623000 | uncertain significance | Hereditary cancer-predisposing syndrome | 2021-07-07 | criteria provided, single submitter | clinical testing | The p.H1252Y variant (also known as c.3754C>T), located in coding exon 22 of the PTCH1 gene, results from a C to T substitution at nucleotide position 3754. The histidine at codon 1252 is replaced by tyrosine, an amino acid with similar properties. This amino acid position is not well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Labcorp Genetics |
RCV003108018 | SCV003781501 | benign | Gorlin syndrome | 2023-05-11 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV003471338 | SCV004206589 | uncertain significance | Basal cell carcinoma, susceptibility to, 1 | 2023-08-15 | criteria provided, single submitter | clinical testing |