Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000000203 | SCV001388246 | pathogenic | Ornithine aminotransferase deficiency | 2023-09-21 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Trp275*) in the OAT gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in OAT are known to be pathogenic (PMID: 1737786, 23076989). This variant is present in population databases (rs267606924, gnomAD 0.0009%). This variant has not been reported in the literature in individuals affected with OAT-related conditions. ClinVar contains an entry for this variant (Variation ID: 180). For these reasons, this variant has been classified as Pathogenic. |
Fulgent Genetics, |
RCV000000203 | SCV002810312 | likely pathogenic | Ornithine aminotransferase deficiency | 2022-03-31 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV000000203 | SCV004208950 | likely pathogenic | Ornithine aminotransferase deficiency | 2023-04-06 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000000203 | SCV000020346 | pathogenic | Ornithine aminotransferase deficiency | 1993-01-29 | no assertion criteria provided | literature only |