Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Department of Pediatrics, |
RCV005054966 | SCV005688644 | likely pathogenic | Renal coloboma syndrome | 2024-12-01 | criteria provided, single submitter | clinical testing | The p.Asn179TrpfsTer17 variant is a novel frameshift variant and is regarded as likely pathogenic (PVS1, PM2, according to ACMG criteria). |