Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000175574 | SCV000227085 | uncertain significance | not provided | 2014-10-10 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000175574 | SCV002207097 | uncertain significance | not provided | 2023-05-13 | criteria provided, single submitter | clinical testing | This sequence change replaces serine, which is neutral and polar, with leucine, which is neutral and non-polar, at codon 162 of the PDE6B protein (p.Ser162Leu). This variant is present in population databases (rs772012465, gnomAD 0.03%). This variant has not been reported in the literature in individuals affected with PDE6B-related conditions. ClinVar contains an entry for this variant (Variation ID: 195056). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt PDE6B protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Dept Of Ophthalmology, |
RCV003888623 | SCV004705747 | uncertain significance | Retinal dystrophy | 2023-10-01 | criteria provided, single submitter | research |