Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000523916 | SCV000618245 | uncertain significance | not provided | 2018-07-19 | criteria provided, single submitter | clinical testing | The S415G variant in the PGK1 gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The S415G variant is not observed in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). The S415G variant is a non-conservative amino acid substitution, which is likely to impact secondary protein structure as these residues differ in polarity, charge, size and/or other properties. This substitution occurs at a position that is conserved across species. In silico analysis predicts this variant is probably damaging to the protein structure/function. We interpret S415G as a variant of uncertain significance |
Fulgent Genetics, |
RCV002476057 | SCV002791592 | uncertain significance | Glycogen storage disease due to phosphoglycerate kinase 1 deficiency | 2022-01-03 | criteria provided, single submitter | clinical testing | |
Mayo Clinic Laboratories, |
RCV000523916 | SCV004225677 | uncertain significance | not provided | 2022-11-18 | criteria provided, single submitter | clinical testing | PM2 |
Labcorp Genetics |
RCV000523916 | SCV004618216 | likely benign | not provided | 2023-10-03 | criteria provided, single submitter | clinical testing |