Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV003265967 | SCV003968153 | uncertain significance | Inborn genetic diseases | 2023-05-02 | criteria provided, single submitter | clinical testing | The c.1034A>G (p.Y345C) alteration is located in exon 4 (coding exon 4) of the PKD2 gene. This alteration results from a A to G substitution at nucleotide position 1034, causing the tyrosine (Y) at amino acid position 345 to be replaced by a cysteine (C). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Juno Genomics, |
RCV004796794 | SCV005416899 | likely pathogenic | Polycystic kidney disease 2 | criteria provided, single submitter | clinical testing | PM2_Supporting+PP3_Moderate+PM5_Supporting+PS4_Supporting+PM6_Supporting+PP4 |