Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute for Human Genetics and Genomic Medicine, |
RCV001814630 | SCV002061324 | uncertain significance | Polycystic kidney disease 2 | 2022-01-20 | criteria provided, single submitter | clinical testing | The detected change has not been reported in the relevant databases (dbSNP151, gnomAD, ClinVar), the renowned PKD database (https://pkdb.mayo.edu) or in the literature. Bioinformatically, a probable effect on the acceptor splice site is predicted by various prediction programs (SSF, MaxEnt, GeneSplicer) for the variant, which could lead to altered splicing and be accompanied by a loss of function of the corresponding protein. However, a reliable classification of the variant is not possible based on the current state of knowledge, so that the variant is currently to be regarded as a “variant of uncertain clinical significance” (ACMG criteria). |
Fulgent Genetics, |
RCV001814630 | SCV005668032 | likely pathogenic | Polycystic kidney disease 2 | 2024-05-22 | criteria provided, single submitter | clinical testing |