Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV000551515 | SCV000631700 | likely benign | Ehlers-Danlos syndrome, kyphoscoliotic type 1 | 2024-01-29 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002314964 | SCV000739524 | likely benign | Familial thoracic aortic aneurysm and aortic dissection | 2017-07-10 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Gene |
RCV001562122 | SCV001784840 | likely benign | not provided | 2020-05-12 | criteria provided, single submitter | clinical testing | |
ARUP Laboratories, |
RCV000551515 | SCV002048016 | uncertain significance | Ehlers-Danlos syndrome, kyphoscoliotic type 1 | 2021-04-29 | criteria provided, single submitter | clinical testing | The PLOD1 c.1582G>A; p.Glu528Lys variant (rs112250644), to our knowledge, is not reported in the medical literature but is reported in ClinVar (Variation ID: 459811). This variant is found in the African/African-American population with an allele frequency of 0.27% (68/24928 alleles) in the Genome Aggregation Database. The glutamate at codon 528 is moderately conserved, and computational analyses are uncertain whether this variant is neutral or deleterious (REVEL: 0.537). Due to limited information, the clinical significance of the p.Glu528Lys variant is uncertain at this time. |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV003330759 | SCV004039247 | uncertain significance | not specified | 2023-08-24 | criteria provided, single submitter | clinical testing | |
Mayo Clinic Laboratories, |
RCV001562122 | SCV004227752 | uncertain significance | not provided | 2022-10-18 | criteria provided, single submitter | clinical testing | BS1 |