Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000486866 | SCV000574214 | likely pathogenic | not provided | 2017-03-23 | criteria provided, single submitter | clinical testing | The S53A variant, present in an alternate transcript of the POU1F1 gene, has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The S53A variant is not observed in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). The S53A variant is a non-conservative amino acid substitution, which is likely to impact secondary protein structure as these residues differ in polarity, charge, size and/or other properties. This substitution occurs at a position that is not conserved. In silico analysis is inconsistent in its predictions as to whether or not the variant is damaging to the protein structure/function. The S53A variant is a strong candidate for a pathogenic variant, however the possibility it may be a rare benign variant cannot be excluded. |
Institute of Human Genetics, |
RCV001253703 | SCV001429552 | uncertain significance | Pituitary hormone deficiency, combined, 1 | 2016-08-19 | criteria provided, single submitter | clinical testing | |
OMIM | RCV001253703 | SCV001934190 | pathogenic | Pituitary hormone deficiency, combined, 1 | 2024-10-10 | no assertion criteria provided | literature only |