Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Hearing and Balance Clinic, |
RCV000474747 | SCV000538186 | pathogenic | X-linked mixed hearing loss with perilymphatic gusher | 2017-03-04 | no assertion criteria provided | clinical testing | The proband and his mother's brother were profound hearing loss since birth , and his mother and father were normal hearing. Then the proband and his mother's brother obtained MRI of inner ear which showed partial cochlear hypoplasia. The genetic analysis showed that the proband and his mother's brother were hemizygous mutation and his mother was carrier of this mutation. |